However, the degree of premature fusion of toes and fingers depends on the severity of the disease. The hands in patients with Apert syndrome always show four common features: a short thumb with radial deviation complex syndactyly of the index, long and ring finger symbrachyphalangism simple syndactyly of the fourth webspace In some of the most critical cases, the person suffering from a genetic disorder develops the fusion of all the toes and fingers. For most children with Apert syndrome, multiple procedures will be required throughout childhood. Learn more about the causes and symptoms. Webbed fingers (syndactyly) in Apert Syndrome is one of the distinguishing features which can affect the quality of the patient’s life, both emotionally and physically, if not corrected surgically. Apert's syndrome • Apert syndrome is a form of acrocephalosyndactyly, a congenital disorder characterized by malformations of the skull, face, hands and feet. Other sutures may also close. Children with this syndrome also have syndactyly, or webbing, of the hands and feet. CARE AND TREATMENT OF APERT SYNDROME The hands of patients with Apert syndrome can be classified into three categories (Upton classi-fication) based on the degree of soft tissue and bone involvement. Syndrome, Apert (acrocephalosyndactyly): An inherited disorder with abnormalities of the skull and face and the hands and feet. fingers and toes, a condition called syndactyly. The hands demonstrate one of the most complex collections of congenital upper limb deformities, posing a significant challenge for the paediatric hand surgeon. Feeding issues, dental abnormalities, hearing loss, hyperhidrosis, and progressive synostosis of multiple bones (skull, hands, feet, carpus, tarsus, and … Apert Syndrome is a condition involving distortions of the head and face and webbing of the hands and feet. It is quite rare and estimates of its incidence vary somewhat, with recent studies placing it between 1 in 65,000 and 1 in 88,000 live births. Children with Apert, Crouzon and Pfeiffer syndrome usually have premature fusion of at least the coronal suture, an opening that extends across the top of the skull. Overview Apert syndrome is a congenital disorder identifiable by birth defects such as an abnormal form of the head and webbed condition of the hands and feet. One of the problems associated with Apert Syndrome is the presence of syndactyly, the fusion of two or more digits both on the hands and the feet. Apert syndrome is a rare, genetic condition in which the joints in a newborn baby’s skull close too early. Apert Syndrome is a congenital condition characterised by primary craniosynostosis, midfacial malformations and complex symmetrical malformations of the hands and feet. Apert syndrome is a relatively uncommon condition that is instantly recognizable on the basis of the pan-syndactylies involving both the hands and feet. Apert syndrome is a rare genetic disorder that causes a fetus’ facial and skull bones to fuse together too early in its development. The hand in Apert syndrome always includes fusion of the middle three digits; the thumb and fifth finger are sometimes also involved. • It is classified as a branchial arch syndrome, affecting the first branchial (or pharyngeal) arch, the precursor of the maxilla and mandible • Disturbances in the development of This is called craniosynostosis. There is premature closure of the sutures of the skull (craniosynostosis). The people with Apert syndrome develop webbed fingers and toes.

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